Isicwangciso sonyango lwe-cerebellar atrophy
Unobangela wesi sifo
1.Imfuzo:
Spinocerebellar ataxia (SCA).
Friedreich's ataxia.
I-Dentatorubral-pallidoluysian atrophy (DRPLA).
2.I-Degenerative:
Iinkqubo ezininzi zohlobo lwe-atrophy C (MSA-C).
3.Ischemic-Hypoxic:
Ityhefu yecarbon monoxide.
4.Ityhefu yeziyobisi:
Phenobarbital sodium.
5.Ukudumba:
Iziphumo ze-cerebelitis ebukhali.
6.Ityhefu yotywala:
Ukwehla kwecerebellar yotywala.
7.Abanye:
I-Paraneoplastic cerebellar degeneration.
IiMbonakaliso zeklinikhi
1.I-Ataxia: I-Ataxia yeyona nto iphambili yokubonakaliswa kwe-cerebellar atrophy. Izigulane zibonisa ukungazinzi ngelixa zimile, zishukuma, kunye nobunzima bokugcina ibhalansi, ngokuqhelekileyo ayikwazi ukuma emlenzeni omnye. Ukuhamba kwawo akuzinzanga, kukho amanyathelo asekelwe ngokubanzi, ukushukuma ecaleni, kunye nemilenze ephezulu egobile kwaye yolulwa ngokungathi iza kuwa. Zinolungelelaniso olulambathayo, kunye neentshukumo ezihlala zigqithisa koko kujoliswe kuko, kwaye nokubhala ngesandla kusenokuhexa kwaye kungalungelelani, kunye noonobumba abakhulu ngokuqhubekayo.
2. I-Cerebellar Dysarthria: Intetho iyacotha, kunye ne-slurred, monotone, kunye ne-nasal tones, efana nephethini efana nokucula. Oku kubangelwa ukungabikho kokulungelelaniswa kwimisipha yokuthetha njengemilebe, ulwimi, kunye ne-pharynx.
3. I-Ocular Motor Disorders: Ekuqaleni kwe-cerebellar atrophy, izigulane zinokufumana i-disconjugate i-gaze kunye ne-oculomotor dysfunction. Basenokuba neenyikima ezirhabaxa zamacala amabini emehlweni, iimeko ezimbalwa ezibonisa i-downbeat okanye i-rebound nystagmus.
I-4.Hypotonia: I-Hypotonia ibonwa ngokuyinhloko kwizilonda ze-cerebellar hemisphere kwaye ayiqhelekanga kwizilonda ezingapheliyo. Nangona kunjalo, kwezinye iimeko ze-cerebellar atrophy, kunokubakho i-hypertonia yemisipha eqhubekayo, efana ne-remor-predominant paralysis.
5.Izibonakaliso ezingezizo iiMoto: Ezi ziquka ukonakala kwengqondo nolwimi. Obunye ubungqina bucebisa unxibelelwano phakathi kwe-cerebellum kunye nokuphazamiseka kwengqondo okufana ne-schizophrenia, i-bipolar disorder, kunye nokuziphatha okukhobokisayo.
Uviwo
1. UVavanyo lweNeurological:
(1) Uvavanyo lweFinger-to-Nose: Yalela isigulana ukuba sandise kwaye sibambe isitho esiphezulu, sithinte impumlo yabo ngencam yomnwe, kwaye siphinde isenzo ngeendlela ezahlukeneyo kunye nesantya, ngamehlo avulekileyo navaliweyo, ethelekisa macala omabini. I-Ataxia ibonakaliswa ngesantya esingahambelaniyo kunye nokuchaneka, ukungaqondi kakuhle, okanye ukufuna ukulungiswa ukuze kufikelelwe kwithagethi. Kwizilonda ze-cerebellar hemisphere, i-ataxia ibonakaliswe ngakumbi kwicala elifanayo njengoko kujoliswe kuyo, ngokuqhelekileyo kugqithise kwithagethi.
(2) Uvavanyo lwe-Heel-to-Shin: Isigulana silala phantsi kwaye senza izenzo ezintathu ngokulandelelana: ukuphakamisa kunye nokwandisa elinye ilungu elingaphantsi, ukubeka isithende kwelinye icala elisezantsi, emva koko isithende phantsi kwe-shin, sijolise ekuchanekeni kwaye iintshukumo ezihambelanayo. Kumonakalo wecerebellar, ukuphakamisa umlenze kunye nokuchukumisa i-shin kunokungazinzi ngenxa yokungaboni kakuhle kunye nokungcangcazela kwenjongo okubangela ukuhla ukuhla.
(3) Uvavanyo lweeMovements ezikhawulezayo ezitshintshayo: Isigulane sibetha ngokukhawuleza ngasemva kwesandla esichaseneyo, okanye senza i-pronation ekhawulezayo kunye neentshukumo ze-supination ze-forearm, okanye zitshintshana ngokuchukumisa itafile ngesundu nangemva kwesandla. Kumonakalo we-cerebellar, iintshukumo zi-clumsy kunye nesingqisho esingaqhelekanga.
(4) Uvavanyo lwe-Rebound: Ngamehlo avaliweyo, elinye ilungu eliphezulu liguqulwa ngamandla kwaye likhutshwe ngumhloli. Kwizilonda ze-cerebellar, ukulungelelaniswa okungahambi kakuhle phakathi kwe-agonist kunye nezihlunu ezichasayo kunokubangela ukunyakaza okugqithisileyo okukhokelela ekuzibetheni. Kungenjalo, zombini iingalo zigcinwe ngaphambili kwaye zandisiwe, kwaye umvavanyi uzityhalela ezantsi ngokukhawuleza aze akhulule. Abantu abaqhelekileyo banokubuyela ngokuchanekileyo kwindawo yokuqala, ngelixa abo bane-cerebellar ataxia abanako ukulawula ukulungelelaniswa phakathi kwe-agonist kunye nezihlunu ezichasayo, ngokuqhelekileyo kubangela ukunyakaza okugqithiseleyo kunye ne-oscillation ende.
5 Uviwo luqhutywa kunye nesigulane esigcina isigxina esiphezulu sandisiwe, okokuqala ngamehlo avulekileyo kwaye avaliwe. Kumonakalo wecerebellar, umnwe wesigulane awukhombe ngokuchanekileyo umnwe womhloli kodwa ugqithise.
(6) Uvavanyo lokuhlala: Isigulana silala phantsi, izandla zibekwe esifubeni ngaphandle kwenkxaso, kwaye uzama ukuhlala. Kubantu abaqhelekileyo, i-trunk kuphela iguquguquka, kwaye zombini imilenze engezantsi inokudandatheka ngaphandle kokushiya ibhedi. Kwizigulane ezinomonakalo we-cerebellar, zombini i-hips kunye ne-trunk flex ngaxeshanye, kwaye zombini imilenze ephantsi iphakamisa, ebizwa ngokuba yi-co-contraction sign.
2.Neuroimaging:
I-CT kunye ne-magnetic resonance imaging (MRI) inokubonisa i-cerebellar atrophy, ebonakaliswe ngokunyuka kunye nokwandiswa kwe-cerebellar fissures, ukunciphisa umthamo, ukubonakala kwe-branched folia, imigodi ye-cerebellar eyandisiweyo, kunye nokwandiswa kwe-ventricle yesine.
Uxilongo
Ukufumanisa i-cerebellar atrophy akusoloko kunzima kwaye ngokuqhelekileyo kusekelwe kwimbali yonyango yesigulana, iimpawu, uviwo lwezonyango, kunye nezifundo zokucinga.






